Adult diagnosis of Swyer-James-Macleods Syndrome-a rare case

Dr Aditya Vora; Dr Supriya Barsode; Dr Deepak Bhosle; Dr Kartik Sharma; Dr Pallav Garg; Dr Mandar Dagade; Dr Dheeraj Agarwal; Dr Mandar Gokate; Dr Babatosh Saha; Dr Amir Mulani

Volume : IX, Issue : II, February - 2019

Adult diagnosis of Swyer-James-Macleods Syndrome-a rare case

Dr Aditya Vora, Dr Supriya Barsode, Dr Deepak Bhosle, Dr Kartik Sharma, Dr Pallav Garg, Dr Mandar Dagade, Dr Dheeraj Agarwal, Dr Mandar Gokate, Dr Babatosh Saha, Dr Amir Mulani

Abstract :

Swyer–James–MacLeod Syndrome (SJMS) is a rare lung condition followed by onchiolitis obliterans occurring in childhood . It is characterized by hypoplasia and/or agenesis of the pulmonary arteries resulting in hypoperfusion of the lung and unilateral hyperlucency on chest radiography . This entity is typically diagnosed in childhood with history of recurrent pulmonary infections but sometimes patients who have little or no symptoms may be missed till adulthood. Symptoms of decreased exercise tolerance, cough ,dyspnoea, and may be confused with onchial asthma ,pulmonary embolism or onchiactasis . Here we presented a 65year–old woman with SJMS discovered on the workup of acute onset eathlessness.