Volume : VIII, Issue : VI, June - 2018

Health–related quality of life in patients of haemophilia from Rajasthan

Dr. Ashish Kavia, Dr. Mrinal Joshi

Abstract :

Introduction: Haemophilia is an X–Linked recessive bleeding disorder affecting men. Haemophilia A & B are defined as severe with the factor level below(<1%), moderate(1–5%), and mild(5–40%). Haemophilia have an impact on the patients quality of life and can affect the everyday life of their families. Quality of life is an important patient based outcome criterion which can be used to describe the impact of the health condition on the patients as well as the effects of the treatment strategies.

Objective:  To analyse health related quality of life (HRQoL) in haemophilia patients

Method:North Indian patients with haemophilia A & B, aged >13yrs were compared with normative individual matched for age, sex, geography and social status. The SF–36 questionnaire used to measure HRQoL, allows to calculate 8 score(on a 0–100 scale)the Physical component (PCS) and Mental component(MCS) summary.Mean Mental (MCS) and physical (PCS) component summary scores were assessed and compared with Indian normative data.

Results:In order to assess HR–QoL in patients with haemophilia A and B , 88 individuals with severe, moderate and mild haemophilia were enrolled out of which  67 patients received MOS short Form 36(SF–36) questionnaire Patients mean age was 21years(SD=9.9), 91% were type A , and 9% were type B,the results from these questionnaire showed that the Mean PCS and MCS was significantly lower in the haemophilia patients compared to the normative data.

Conclusion:patients with haemophilia have poor health related quality of life as compared to normative individual. That’s why early intervention in haemophilia is must to reduce the functional disability. These observations should help to optimise health care delivery in this increasing and neglected population of people with haemophilia.

Keywords :

Article: Download PDF   DOI : 10.36106/ijar  

Cite This Article:

Dr. Ashish Kavia, Dr. Mrinal Joshi, Health–related quality of life in patients of haemophilia from Rajasthan, INDIAN JOURNAL OF APPLIED RESEARCH : Volume-8 | Issue-6 | June-2018

Number of Downloads : 280

References :