HOLOCORD SYRINX PRESENTING AS BILATERAL PTOSIS.A CASE REPORT

Nihar Ranjan Biswal; Asok Kumar Mallick; Geeta Mohanty; Kali Prassanna Swain; Srikanta kumar Sahu; Lulup kumar Sahoo

Volume : V, Issue : III, March - 2015

HOLOCORD SYRINX PRESENTING AS BILATERAL PTOSIS.A CASE REPORT

Nihar Ranjan Biswal, Asok Kumar Mallick, Geeta Mohanty, Kali Prassanna Swain, Srikanta Kumar Sahu, Lulup Kumar Sahoo

Abstract :

INTRODUCTION Horner’s syndrome,along with weakness and atrophy of hand as well as anaesthesia to pain and temperature is a well recognized finding in a case of syringomyelia.Few cases have been published as horner’s syndrome as a presenting feature of chairy–1 malformation with syringomyelia.We report a case of 22yr female presenting with bilateral ptosis probably part of syringomyelia with wekness and atrophy of both upper limbs with out any sensory findings such as loss of pain and temperature sensation having chiary–1 malformation and syringomyelia on imaging. Case reportWe report a case of 22year female patient with chiary–1 malformation and syrinx upto 9th thoracic vertea level.who presented with bilateral ptosis along with weakness and wasting of both small muscles of hand and forearm .Typical neurological signs and symptoms of syringomyelia like anaesthesia to pain and temperature was absent in this case. Though horner’s syndrome is described but only bilateral ptosis without anhydrosis and miosis is a rare finding Conclusion–possibility of a syringomyelia could be thought in patients presenting with only ocular findings like progressive ptosis with upper limb wasting even if in the absence of classical sensory manifestation of syrinx.