Volume : X, Issue : VIII, August - 2020

INTESTINAL LYMPHANGIECTASIA IN CHILDREN (ILC)

Dr. Sujay Chaudhuri

Abstract :

BACKGROUND Primary Intestinal Lymphangiectasia (PIL) is a rare cause of protein losing enteropathy in children. To evaluate incidence, clinical and investigational profile and treatment outcome of PIL in children, the following study was conducted in a tertiary care center of North India. METHOD The children who attended pediatric gastroenterology OPD of PGIMER, Chandigarh from July 1993 to June 2003, with features of PIL, have adjusted. History, clinical examination, investigations (complete blood count, LFT, Lipid profile, USG whole abdomen, UGI Endoscopy, colonoscopy, immunoglobulins etc.) were reported. Secondary cause are carefully executed by echocardiography, wmc examination, CT are done depending upon causes. The patients were given low fat, high protein diet, MCT oil, octreotide, TPN etc. the patients were followed up till improvement of clinical figure and symptoms. RESULTS Five children (age 1 – 3 years) were admitted in pediatric gastroenterology ward of PGIMER from July 1993 to June 2003 with clinical feature of PIL. Bilateral pedal pitting edema of feet was present in all cases. USG whole abdomen showed thickened small bowel wall with dilating of loops in all cases. Central abdominal swelling, ascites was present in 4 cases. Severe mesenteric edema was present in 3 cases. Endoscopic abnormalities were scattered white plaques a presence of chyle like substances covering mucosa in all 5 cases. All 5 cases had located lesions in duodenum, upper jejunum. CT imaging should defuse modular small bowel wall thickening and edema, small bowel wall dilatation, “halo sign” lesions were patchy and restricted to duodenum and upper jejunum. Scintigraphy was not done. All 5 patients were gone diet modification, MCT oil, both enteral and praenteral nutrition. All responded very well to conservative management. Nobody needed surgery, lymphocytes, immunoglobulin, seen albumin which were care initially were restored to normal volume often treatment. CONCLUSION :– Primary intestinal lymphangiectasia (PIL) is rare but potential came of protein losing enteropathy. After careful exclusion of secondary cases PIL showed be properly investigated and management so that long term outcome becomes good.

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Article: Download PDF    DOI : 10.36106/ijar  

Cite This Article:

INTESTINAL LYMPHANGIECTASIA IN CHILDREN (ILC), Dr. Sujay Chaudhuri INDIAN JOURNAL OF APPLIED RESEARCH : Volume-10 | Issue-8 | August-2020

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