Klippel Trenaunay Syndrome with Angiokeratoma–A case report with brief review of the literature.

Dr. Meenal Patil; Dr. Manoj N. Kulkarni

Volume : V, Issue : II, February - 2015

Klippel Trenaunay Syndrome with Angiokeratoma–A case report with brief review of the literature.

Dr. Meenal Patil, Dr. Manoj N. Kulkarni

Abstract :

Klippel Trenaunay Syndrome is a sporadic disorder presenting at birth, childhood or in early adult life , consisting of a triad of cutaneous , vascular & soft tissue involvement. It may have a mild to severe form of disease with life– threatening bleeding manifestations. It usually affects one extremity and may have associated vascular lesions such as angiokeratomas. We report a case of multiple angiokeratomas in Klippel Trenaunay syndrome in an 8 –year old girl.