LADY WITH A BIG HEART: ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA

Dr. Kavita Krishna; Dr. SachinAdukia; Dr. Manasi Korde; Dr. ChandrakantChavan; Dr. VaibhavLotke

Volume : V, Issue : II, February - 2015

LADY WITH A BIG HEART: ARRHYTHMOGENIC RIGHT VENTRICULAR DYSPLASIA

Dr. Kavita Krishna, Dr. Sachinadukia, Dr. Manasi Korde, Dr. Chandrakantchavan, Dr. Vaibhavlotke

Abstract :

Arrhythmogenic right ventricular dysplasia (ARVD) is characterized by fiofatty replacement of myocardium which affects mainly the right ventricle. While it is one of the rare forms of cardiomyopathies, it is the second most common cause of sudden death of young adults world–wide (after hypertrophic cardiomyopathy–obstructive type), causing up to 20% of sudden cardiac deaths in patients less than 35 years of age. Incidence of ARVD is unknown in the Indian population. A rare case of ARVD is reported. Isolated dilatation of right ventricle with significant trabeculations and pseudosacculations, ECG showing RBBB with epsilon waves and chest x– ray suggestive of gross cardiomegaly make it an interesting case.