Management of combined hamarthoma of the retina and retinal pigment epithelium:clinical, surgical with combined intravitreal/retrobulbar injections  and rehabilitation results

Raffaele Nuzzi; Carlo Lavia; Roberta Spinetta

Volume : VII, Issue : IX, September - 2017

Management of combined hamarthoma of the retina and retinal pigment epithelium:clinical, surgical with combined intravitreal/retrobulbar injections and rehabilitation results

Raffaele Nuzzi, Carlo Lavia, Roberta Spinetta

Abstract :

This case report describes the case of a 7 years old patient with exotropia and monolateral combined amarthoma of the retina and retinal pigment epithelium(CHRRPE) treated with a combined surgical and rehabilitative method.

The patient underwent a vitrectomy plus memanes peeling and three off label Bevacizumab intravitreal injections plus retrobulbar Triamcinolone injections. After the first Bevacizumab–Triamcinolone injection the Retimax vision trainer rehabilitation method started.

Macular edema (central retinal thickness from 472 to 307µm) ,lesion height (from 805 to 490µm) and lesion vascularization decreased together with a slight improvement in visual function both in terms of visual acuity ( BCVA from 6/60 to 6/24 ) and retinal sensibility at microperimetry (from 12 dB to 18.2 dB).

OCT and Angio–OCT are useful tools to assess the features of the lesion so to plan the best treatment and a prompt amblyopia treatment is mandatory to achieve the best functional outcome in each case.