PEDIATRIC MOYA MOYA SYNDROME WITH FAMILIAL HISTORY AND ENCEPHALO DURO ARTERIO MYO SYNANGIOSES. – A Rare Case Report.

Dr. Sudhir Suggala; Dr. Jayanth kumar Tiramdasu; Dr. Velagapudi Murali

Volume : X, Issue : II, February - 2020

PEDIATRIC MOYA MOYA SYNDROME WITH FAMILIAL HISTORY AND ENCEPHALO DURO ARTERIO MYO SYNANGIOSES. – A Rare Case Report.

Dr. Sudhir Suggala, Dr. Jayanth Kumar Tiramdasu, Dr. Velagapudi Murali

Abstract :

Moya Moya disease (MMD) is a type of chronic cereovascular occlusion disease, which frequently occurs in East Asian populations, including pediatric and adult patients, and may lead to ischemic or hemorrhagic stroke, headache, epilepsy or transient ischemic attack. To date, the underlying mechanisms of MMD have remained to be fully elucidated, but certain studies have indicated that genetic factors may be an essential component of its development. Cereal angiography is the best approach for diagnosing MMD. However, with technological advances, non–invasive techniques are increasingly used to accurately evaluate MMD. MMD is commonly treated via surgery, and an increasing number of patients are benefitting from the intra– and extra–cranial revascularization. The present article provides a case report of a pediatric moyamoya disease