Primary orbital peripheral neuroectodermal tumour – A rare presentation.

Dr. Ashok Madan; Dr. Mona Deshmukh; Dr. Samreen Ayubi

Volume : VII, Issue : X, October - 2017

Primary orbital peripheral neuroectodermal tumour – A rare presentation.

Dr. Ashok Madan, Dr. Mona Deshmukh, Dr. Samreen Ayubi

Abstract :

Primitive neuroectodermal tumor(PNET) is a small round cell malignant tumor of neuroectodermal origin. Most of the PNET’s occur in the central nervous system. Those occurring outside are called peripheral PNET(pPNET). We report a case of an adult male presenting with eccentric proptosis with extraconal and intraconal mass, diagnosed as malignant round cell tumor on histopathology and pPNET on immunohistochemistry.