PROTEUS SYNDROME WITH SPLENIC CYSTS

G.Eswar; D.Srinivasa Rao; B.Madhava Rao; R.Ravi Ram; K.Ramalakshmi; S.Nandini; Dr Aswini Kumar Sahoo

Volume : VIII, Issue : III, March - 2018

PROTEUS SYNDROME WITH SPLENIC CYSTS

G. Eswar, D. Srinivasa Rao, B. Madhava Rao, R. Ravi Ram, K. Ramalakshmi, S. Nandini, Dr Aswini Kumar Sahoo

Abstract :

Complex hamartomatous Proteus Syndrome was characterized by multiple diverse somatic manifestations. We present a case with skeletal, soft tissues, skin and vascular lesions but with unusual rare finding of splenomegaly with multiple cysts, spå the Central Nervous System. On a careful review of Indian literature on the subject, there have been no prior documentation of Proteus Syndrome with splenic cysts.