RETROPANCREATIC FOLLICULAR DENDRITIC CELL SARCOMA: A DIAGNOSTIC CHALLENGE

Gunjan S Desai; Verushka Chhabra; Rajiv C Shah; Pravin Mahajan; Chandralekha Tampi; Palepu Jagannath

Volume : VII, Issue : VII, July - 2017

RETROPANCREATIC FOLLICULAR DENDRITIC CELL SARCOMA: A DIAGNOSTIC CHALLENGE

Gunjan S Desai, Verushka Chhabra, Rajiv C Shah, Pravin Mahajan, Chandralekha Tampi, Palepu Jagannath

Abstract :

Follicular dendritic cell sarcoma [FDCS] is a rare nodal or extranodal soft tissue tumor, uncommon in retropancreatic node. Etiopathogenesis of the disease is not clear and it is often misdiagnosed. Presentation is usually incidental. Imaging and histopathology features can be confusing. A high index of suspicion and a specific approach to diagnosis is of utmost importance. Immunohistochemistry is a must for diagnosis. CD 21 and CD 23 are specific for FDCS. Management is by complete resection. The role of chemotherapy and radiation is not clear. We report a case of retropancreatic FDCS and iefly review our approach to its management.