Volume : IV, Issue : I, January - 2014

Sickle ? thalassaemia with hypersplenism & crisis, a rare occurrence

Dr. Kurundkar Gajanan Balaji, Dr. Patel Rishi Devilal

Abstract :

Sickle β thalassaemia is a heterogeneous disorder with a variable clinical expression ranging from a symptomless state to a condition indistinguishable from homozygous sickle cell anemia. Sickle β thalassaemia is generally thought to represent the milder end of the spectrum of sickle cell syndromes. We describe a case 13 years/female having sickle β thalassaemia with hypersplenism who also had crisis illustrating that sickle β thalassaemia may run an unexpected clinical course. Sickle β thalassaemia is due to the interaction between HbS and the mild form of β thalassaemia which has an inhibitory effect on red cell sickling due to HbA.¹ However, it is important to emphasize that serious complications may occur unexpectedly as is shown by our patient. This makes the case important to report.

Keywords :

Article: Download PDF   DOI : 10.36106/ijar  

Cite This Article:

Dr. Kurundkar Gajanan Balaji, Dr. Patel Rishi Devilal Sickle ? thalassaemia with hypersplenism & crisis, a rare occurrence Indian Journal of Applied Research, Vol.IV, Issue. I

Number of Downloads : 617

References :