STURGE–WEBER SYNDROME– A LITERATURE REVIEW

Dr. Sanjeev kumar pandey; Dr. Prakash kumar; Dr. Rajiv Sinha

Volume : VI, Issue : II, February - 2016

STURGE–WEBER SYNDROME– A LITERATURE REVIEW

Dr. Sanjeev Kumar Pandey, Dr. Prakash Kumar, Dr. Rajiv Sinha

Abstract :

The Sturge–Weber syndrome, also known as encephalofacial angiomatosis, is a rare neurocutaneous disorder that occurs as a sporadic congenital condition. It is characterized by a port wine stain that affects the skin in the distribution of the ophthalmic anch of the trigeminal nerve and is associated with venouscapillary abnormalities of the leptomeninges and the eye. It may be suspected in a child presenting with seizure and a characteristic skin lesion along trigeminal nerve distribution. The chacteristic features on computed tomography and magnetic resonance imaging lead to the diagnosis. The goal of therapy is centred around controlling the seizures.