Surgical patch closure of Right Pulmonary Artery to Left Atrium Fistula – A rare entity with common clinical presentation.

Dr. Lata Khatnani Koneru; Dr. Anurag Rai; Dr. Subhash S. Rajput

Volume : VIII, Issue : VIII, August - 2018

Surgical patch closure of Right Pulmonary Artery to Left Atrium Fistula – A rare entity with common clinical presentation.

Dr. Lata Khatnani Koneru, Dr. Anurag Rai, Dr. Subhash S. Rajput

Abstract :

Direct fistulous communication of the right pulmonary artery and the left atrium is a rare congenital malformation of the pulmonary vasculature. It presents as either central cyanosis or its complications and heart failure specially in newborn.Intervention (whether transcatheter or surgical) is usually determined by the anatomy, location and type of the fistula. This report illustrates a case of aneight year old male child presented with cyanosis and dyspnoea, diagnosed to have Right Pulmonary Artery to Left AtriumFistula with large Atrial Septal Defect on various imaging studies. Location of fistula opening was near left pulmonary veins.In this scenario Transcatheter closure can cause pulmonary vein obstruction hence Surgical repairwas opted and done successfully.